Treatmentapproaches to Cleidocranial Dysostosis: a Review and a Case Report
نویسندگان
چکیده
Cleidocranial dysostosis is a generalized skeletal dysplastic condition and primarily affects the development of the bones and teeth. The genetic etiology lies on chromosome number 6p21, core binding factor (CBFA1). This paper explains the treatment procedure carried out for a sixteen year old female patient diagnosed with cleidocranial dysostosis. Therapy includes surgical removal or exposure of impacted teeth, extraction of supernumerary teeth along with orthodontic treatment.
منابع مشابه
Cleidocranial dysostosis--a case report and review of the literature.
Cleidocranial dysostosis is a generalised dysplasia of bone and teeth with predominantly autosomal dominant inheritance. A new case referred to the Paediatric Department at the British Military Hospital, Rinteln is reported and a review of the literature discussed.
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